Pulmonary Manifestation of Primary Immunodeficiency Disease

Primary immunodeficiency diseases (PIDs) are a heterogeneous group of disorders,

characterized by increased susceptibility of infections, mainly in respiratory system. More than 400 different PIDs have already been recognized and classified into

8 groups. Many patients with PIDs firstly present with upper and lower respiratory

tract manifestations, while delay in diagnosis can lead to morbidity and even mortality of affected patients. Our understanding on PIDs is rapidly improving, which

helps us in making definite diagnosis managing more efficiently.

This book is an attempt to gather the most recent advances in pulmonary problems of patients with PIDs, where diagnosis and management of pulmonary manifestations have also been discussed